選択的IgA低下症を伴った巨大肝海綿状血管腫の1例

概要

論文の詳細を見る
A 42-year-old woman was admitted to the hospital because of hepatomegaly of a few years' duration. About a month before admission, she came to our hospital because of retinal bleeding. Although hematological test and liver function were almost normal, 99mTc liver scintigram revealed a massive defect in the right lobe. After the admission, a giant hemangioma of the right lobe was confirmed by selective celiac arteriography. It was also noted that serum IgA level markedly decreased, wherease secretory IgA level and IgA containing cells in the intestinal mucosa were within normal limit. After the tumor Was successfully resected, serum IgA level rapidly increased to normal range, and remained normal for 11 months. From these result, it is speculated that the cause of selective hypoIgA of this case is the comsumption of it by the hemangioma.
社団法人日本肝臓学会の論文