Lengthy Diagnostic Challenge in a Rare Case of Pulmonary Veno-Occlusive Disease: Case Report and Review of the Literature
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概要
- 論文の詳細を見る
Pulmonary veno-occlusive disease (PVOD) is a rare and usually survival poor disorder. We report a patient with a long history of progressive dyspnea of over 8 years, who with a diagnosis of chronic cor pulmonale confirmed elsewhere, was ultimately diagnosed as PVOD via histological analysis of a lung biopsy. After treatment with combined bosentan, diuretics and digoxin, his symptoms and function improved. This case highlights that PVOD is an under-recognised and often misdiagnosed disease, especially in its chronic form. Understanding its pathogenesis, its poor response to medical therapy and its dismal prognosis remain challenges for the treatment of PVOD.
- 社団法人 日本内科学会の論文
著者
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Guo Feng
Department of Materials Science, Fudan University, 220 Handan road, Shanghai, 200433, P. R. China
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Yan Chun-song
Department of Respiratory Diseases, the Second Affiliated Hospital of Nanchang University, China
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Zhang Xin-yi
Department of Respiratory Diseases, the Second Affiliated Hospital of Nanchang University, China
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Kuang Jiu-long
Department of Respiratory Diseases, the Second Affiliated Hospital of Nanchang University, China
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Ye Xiao-qun
Department of Respiratory Diseases, the Second Affiliated Hospital of Nanchang University, China
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Cai Yin
Department of Respiratory Diseases, the Second Affiliated Hospital of Nanchang University, China
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Guo Feng
Department of Respiratory Diseases, the Second Affiliated Hospital of Nanchang University, China
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