Immunoglobulin light-chain (AL) amyloidosis with myasthenic symptoms and echocardiographic features of dilated cardiomyopathy
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概要
- 論文の詳細を見る
Myasthenic symptoms and the echocardiographic findings of dilated cardiomyopathy are very rare in primary AL amyloidosis. We report a 59yearold man with dyspnea on effort and weakness after exercise. His electrocardiogram showed ischemic heart disease and echocardiography indicated dilated cardiomyopathy. Muscle biopsy revealed amyloidosis with deposits of lambda light chainderived amyloid within the vessel wall. Treatment with PGE1 resulted in improvement of the myasthenic symptoms. This patient indicates that myasthenic symptoms and dilated cardiomyopathy would be a unique syndrome associated with systemic AL amyloidosis involving mainly the small vessels, i.e., AL amyloid angiopathy, in the skeletal muscles and myocardium vessels.
- The Japanese Society of Internal Medicine = 日本内科学会の論文
著者
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Yoshita Mitsuhiro
Department Of Neurology And Neurobiology Of Aging Kanazawa University Graduate School Of Medical Sci
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Yamada Masahito
Department Of Neurology & Neurobiology Of Aging Kanazawa University Graduate School Of Medical S
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Yamada Masahito
Department of Neurology and Center for Neuroscience, University of California at Davis
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Yoshita Mitsuhiro
Department of Neurology and Neurobiology of Aging, Kanazawa University Graduate School of Medical Science
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Ishida Chiho
Department of Neurology and Center for Neuroscience, University of California at Davis
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Yanase Daisuke
Department of Neurology and Center for Neuroscience, University of California at Davis
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