Heredity in Multiple System Atrophy
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概要
- 論文の詳細を見る
We investigated the family histories of 157 Japanese patients with probable orpossible multiple system atrophy (MSA). A family history of neurodegenerativedisorders was only detected in three MSA patients (1.9%). We evaluated these patientsby careful neurological examination, neuroimaging studies, and genetic studies toexclude hereditary spinocerebellar ataxia with a similar clinical phenotype to MSA. Theresults indicated that one of them had a family history of MSA. Although the familialpresence of neurodegenerative disorders is rare in MSA patients, the existence of suchcases suggests that MSA may have a genetic background.
- Elsevier B.V.の論文
- 2006-01-15
著者
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Sugiura Hiroshi
Department Of Surgical Oncology Division Of Cancer Medicine Hokkaido University Graduate School Of M
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TAKEI Asako
Hokuyukai Neurology Hospital
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Sasaki Hidenao
Department Of Neurology Graduate School Of Medicine Hokkaido University
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