Electrocardiographic and Clinical Characteristics of Idiopathic Restrictive Cardiomyopathy in Children
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概要
- 論文の詳細を見る
Background Idiopathic restrictive cardiomyopathy (RCM) is not a single disease and is rare. Methods and Results The clinical features and clinical course of 12 pediatric patients with RCM seen between 1978 and 2005 were retrospectively analyzed. The age at diagnosis ranged from 4 months to 12 years (median 4 years). The age of 7 patients diagnosed because of an abnormal electrocardiogram (ECG) ranged from 4 to 12 years. Three infants less than 2 years old presented with cardiomegaly. Obliquely elevated ST-T segments and the late peak T waves on 12-lead ECG were present in 8 patients (67%). Three patients with ST depression during exercise had no perfusion defects on radioisotope myocardial perfusion imaging. Two patients underwent orthotopic heart transplantation. Of the remaining 10 patients, 7 have died : 4 died suddenly and 3 died of right heart failure. Three patients with a hypertrophic left ventricular wall had a prolonged survival. The probability of survival at 1, 2 and 3 years was 78%, 52% and 26%, respectively. Conclusions Obliquely elevated ST-T segments and the late peak T wave on ECG are characteristic, and reflect the restrictive physiology, which may indicate abnormalities of repolarization of ventricular muscle. The mode of death was either heart failure from pulmonary hypertension or sudden death from presumed ventricular arrhythmia.
- 社団法人日本循環器学会の論文
- 2007-09-20
著者
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Ueda Hatsue
Department of Pathology, National Cardiovascular Center
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Ueda Hatsue
Department Of Cardiology National Cardiovascular Center
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Echigo Shigeyuki
Department of Pediatrics, National Cardiovascular Center
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Yamada Osamu
Department Of Pediatric Cardiology Division Of Cardiology National Cardiovascular Center
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TSUDA Etsuko
Department of Pediatrics, National Cardiovascular Center
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Kurosaki Ken-ichi
Department Of Pediatric Cardiology Division Of Cardiology National Cardiovascular Center
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Yamada Osamu
Department Of Cardiovascular Dynamics National Cardiovascular Center Research Institute
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Kurosaki Kenichi
Department of Pediatric Cardiology, National Cardiovascular Center
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Hayashi Tamaki
Department of Pediatrics, National Cardiovascular Center
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Tsuda Etsuko
Department Of Pediatric Cardiology National Cardiovascular Center
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Echigo Shigeyuki
The Japanese Society of Pediatric Cardiology and Cardiac Surgery Joint Working Groups
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Yamada Osamu
Department Of Pediatrics National Cardiovascular Center
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Echigo Shigeyuki
Department Of Pediatrics Nara Medical University
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Echigo Shigeyuki
Department Of Pediatrics National Cardiovascular Center
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Echigo Shigeyuki
Department Of Pediatric Cardiology National Cardiovascular Center
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Hayashi Tamaki
Department Of Pediatrics Nara Medical University
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Echigo Shigeyuki
Department Of Pediatrics Cardiac Surgery National Cardiovascular Center Osaka.
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Echigo Shigeyuki
Pediatrics National Cardiovascular Center
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Kurosaki Ken-ichi
Department Of Pediatrics National Cardiovascular Center
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