左上大静脈の左房還流舶x静脈還流異常を伴った総動脈幹症II型の1例

概要

論文の詳細を見る
A l-year-3-month old girl who had Persistent Truncus Arteriosus (Type II) was operated on using the Hancock 14 mm diameter valved conduit under the deep hypothermia, circulatory arrest and limited cadio-pulmonary bypass. Post-operatively, unexpected right to left intracardiac shunt was found and the patient developed severe heart failure. On the 1-st post-operative day, emergency cardiac catheterization and angiography demonstrated PLSVC draining into the left atriurn and right upper and middle PAPVC into right SVC. Under the cardio-pulmonary bypass with hypothermic low flow perfusion technique, an intraatrial repair was carried out immediately. Despite of the total repair, patient died of severe heart failure on the second post-operative day. Anatomical findings at autopsy were:Persistent Truncus Arteriosus (Type II) associated PLSVC draining into the left atrium, bilateral PAPVC (right upper & middle PV into right SVC and left upper PV into the coronary sinus), a small ASD and PDA. The incidence, diagnosis and surgical technique of this rare anomaly are discussed with some literatual considerations.
日本小児外科学会の論文
1983-06-20