Dilated Cardiomyopathy in Kugelberg-Welander Disease : Coexisting Sleep Disordered Breathing and Its Treatment with Continuous Positive Airway Pressure
スポンサーリンク
概要
- 論文の詳細を見る
A rare complication of possible secondary dilated cardiomyopathy to Kugelberg-Welander disease was described in a 53-year-old patient with this inherent motor neuron disease, whom we diagnosed after a genetic analysis of the defective survival motor neuron gene. An association of sleep disordered breathing of Cheyne-Stokes respiration was diagnosed, which was virtually eliminated with continuous positive airway pressure via nasal mask. Considering the paucity of therapeutic options in most degenerative neuromuscular disorders, ameliorations in not only sleep quality but also cardiac function with continuous positive airway pressure have clinical implications.
- 社団法人 日本内科学会の論文
- 2004-10-01
著者
-
Kuru Satoshi
Department of Neurology, National Hospital Organization Suzuka National Hospital
-
YASUMA Fumihiko
Department of Cardiology, Nagoya University Graduate School of Medicine
-
Yasuma Fumihiko
Department Of Cardiology Nagoya University Graduate School Of Medicine
-
Kuru Satoshi
Department Of Neurology Suzuka National Hospital
-
Yasuma Fumihiko
Department Of Internal Medicine Suzuka National Hospital
-
KONAGAYA Masaaki
Department of Neurology, Suzuka National Hospital
-
Konagaya Masaaki
Department Of Neurology Suzuka National Hospital
-
Konagaya Masaaki
Department Of Neurology National Suzuka Hospital
-
Yasuma Fumihiko
Department of Cardilogy, Nagoya University, Graduate School of Medicine
関連論文
- Carvedilol can Prevent Cardiac Events in Duchenne Muscular Dystrophy
- Continuous Positive Airway Pressure Improves Daytime Baroreflex Sensitivity and Nitric Oxide Production in Patients with Moderate to Severe Obstructive Sleep Apnea Syndrome
- PE-310 Low Plasma BNP in Patients with Duchenne Muscular Dystrophy is Associated with Preserved Diastolic Function and Low Systemic Vascular Resistance(Cardiomyopathy, basic/clinical-5, The 71st Annual Scientific Meeting of the Japanese Circulation Societ
- -361-EFFECTS OF EPICARDIAL PACING ON ENDSYSTOLIC PRESSURE VOLUME RELATION : Ventricular Function : FREE COMMUNICATIONS(II) : PROCEEDINGS OF THE 53th ANNUAL SCIENTIFIC MEETING OF THE JAPANESE CIRCULATION SOCIETY
- -101- THE EFFECTS OF VASODILATING AGENTS ON VENOUS TONE IN VIVO IN THE DOG : Pulmonary Circulation, Papillary Circulation : FREE COMMUNICATIONS(I) : PROCEEDINGS OF THE 51th ANNUAL SCIENTIFIC MEETING OF THE JAPANESE CIRCULATION SOCIETY
- ASSESSMENT OF THE INDEXES OF THE LEFT VENTRICULAR ISOVOLUMIC RELAXATION FORM PRESSURE FALL : Ventricular Function : PROCEEDINGS OF THE 50th ANNUAL SCIENTIFIC MEETING OF THE JAPANESE CIRCULATION SOCIETY
- -347-THE ANALYSIS OF IN VIVO VENOUS TONE IN DOGS
- -346-HEMODYNAMIC AND RESPIRATORY STATUS DURING DIAPHRAGM PACING
- Activities of Daily Living, Functional Capacity, and Life Satisfaction of Subacute Myelo-Optico-Neuropathy Patients in Japan
- Home Oxygen Therapy and Sleep Quality of Heart Failure Patients(Letter to the Editor)
- An autopsy case of spinal muscular atrophy type III (Kugelberg-Welander disease)
- Aortic Pressure Augmentation as a Marker of Cardiovascular Risk in Obstructive Sleep Apnea Syndrome
- PE-309 Cardiac Myolysis and LV Dysfunction in Patients with Duchenne Muscular Dystrophy(Cardiomyopathy, basic/clinical-5, The 71st Annual Scientific Meeting of the Japanese Circulation Society)
- Recording of electroencephalograms and electrocardiograms during daytime sleep in trained canines : Preparation of the sleeping dogs
- REM Sleep is Impaired by a Small Amount of Alcohol in Young Women Sensitive to Alcohol
- Pericardioperitoneal Drainage
- Should Cardiologists Treat Cheyne-Stokes Respiration and Congestive Heart Failure With Oxygen, Bi-Level/Continuous Positive Airway Pressures or Drugs Alone?
- Dilated Cardiomyopathy in Kugelberg-Welander Disease : Coexisting Sleep Disordered Breathing and Its Treatment with Continuous Positive Airway Pressure
- Age Related Differences in Electroencephalographic and Cardiac Arousal at the Termination of Sleep Apnea/Hypopnea
- Prognosis of the middle-aged and aged patients with obstructive sleep apnea syndrome
- BREATHING ABNORMALITIES DURING SLEEP IN PATIENTS WITH CHRONIC HEART FAILURE
- Homozygosity and linkage disequilibrium mapping of autosomal recessive distal myopathy (Nonaka distal myopathy)
- Autopsy case of hereditary spastic paraplegia with thin corpus callosum showing severe gliosis in the cerebral white matter
- Change in Activities of Daily Living, Functional Capacity, and Life Satisfaction in Japanese Patients with Subacute Myelo-Optico-Neuropathy
- Decreased resting energy expenditure in patients with Duchenne muscular dystrophy
- Factors Contributing to Sleep Disturbance and Hypnotic Drug Use in Hemodialysis Patients
- Preoperative Management of Deteriorating Mitral Regurgitation and Heart Failure with Continuous Positive Airway Pressure