小児におけるpure red cell anemiaの4例とその治療の検討

概要

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Treatment for 4 cases of pure red cell anemia was discussed. Three cases of them were congenital hypoplastic anemia (Blackfan-Diamond) and the other was acute erythroblastopenia (Gasser).Cases with congenital hypoplastic anemia fairly well responded to corticosteroid therapy which was given continuously, intermittently or temporalily.The exellent result was obtained in the case, in which the treatment was begun at 7 month old, immediately after diagnosis was made, resulting in sufficient remission for last 2 years with intermittent administration of corticosteroid.Although one patient revealed temporaly improvement for 3 months with blood transfusion alone, corticosteroid therapy was generally required to maintain remission in cases with congenital hypoplastic anemia.
一般社団法人日本血液学会の論文