A Case Report of Pathological Dislocation of the Hip in von Recklinghausen's disease.

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A rare case of pathological dislocation of the hip in von Recklinghausen's disease is reported.A 13-year-old boy suddenly developed pain and dislocation of his right hip with no obuious cause. He visited our department 8 months after onset of symptoms for right hip pain and a limp. He had many typical café au lait spots on his skin and bilateral anterior leg angulation. Neurofibroma were detected by skin biopsy. Radiographs demonstrated right femoral head deirtion to the supra-lateral side, t femur was atrophic femur and both acetabula were hypoplastic. Joint effusion of the right hip was seen on MR I and arthrtgraphy. CT showed hypoplasia of both acetabul a and an irregular margin of the right acetabulum with bone multiplication. We proposed that this pathological dislocation was caused by decreasing restriction and congruity of the hip joint. The former is due to relaxation of the joint capsle, and the latter is due to the irregular acetabular surface caused by invasion of neurofibroma.
西日本整形・災害外科学会の論文