Abnormalities of jaw and face in patients with Hajdu-Cheney syndrome.

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Since Hajdu et al in 1948 and Cheney et al in 1965 reported that Hajdu-Cheney syndrome is a disease showing acro-osteolysis, cranial deformity, Wormian bone, malformation of frontal sinus, basilar impression, osteoporosis, etc., only 29 cases have been reported including the personal case (J. Kawamura et al.: J. Neuroradiology 21: 295-301 1981) so far. This time, we studied about the findings of jaw and face of patients who were diagnosed as Hajdu-Cheney syndrome in the Department of Neurology and Internal Medicine of our hospital, and report its outlines as follows.<BR>Patient: A 25-year-old male. Chief complaint: Trembling of the teeth and difficulty of chewing in 3+3/5+5. Date of the initial examination: October 3, 1983.<BR>The finding of oral cavity noted the trembling of the teeth in 35-4;35 The cleaning of oral cavity was extremely unfavorable, and odontolithiasis with high degree was noted in 7+7/7+7 in 3+3/5+5. The cleaning of oral cavity was extremely unfavorable, and odontolithiasis with high degree was noted in 7+7/7+7 Anterior ejected disease of lower jaw was noted in overjet-4 mm and overbite-2mm. X-rays finding: By panorama X-rays, absorption picture of bone, taurodontia and impacted teeth were observed in 7+7/7+7, and, respectively. No characteristic findings were noted in X-rays of head region, vertebral column, upper limb and lower limb, and CT scan.
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