Caroli 病の1剖検例

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A 26 year-old man was admitted to our hospital because of a right hypochondralgia and a high fever, A diagnosis of congenital cystic dilatation of intrahepatic bile ducts (Caroli's disease) was made. Although the patient underwent a right lobectomy of the liver, he died 3 months after the operation. The surgically resected liver and the autopsied liver were investigated and compared in details.<BR>Microscopically, hyperplastic epithelium of the cystic dilated bile ducts and proliferated, bizarre bile ducts in the portal areas with moderate fibrosis and slight inflammatory change were observed. Renal tubular ectasia was also observed in the bilateral kidneys.<BR>In this paper, we discussed the relationship between Caroli's disease, congenital hepatic fibrosis and choledochal cyst, and reviewed 35 cases reported in the literature.
社団法人日本肝臓学会の論文