Rhabdomyosarcoma in the Inferior Vena Cava with Secondary Budd-Chiari Syndrome.
スポンサーリンク
概要
- 論文の詳細を見る
A 63-year-old man with symptoms of obstruction of the inferior vena cava was examined by computed tomography, ultrasound imaging and angiography. Examination revealed a tumor in the inferior vena cava, and transvenous biopsy revealed a rhabdomyosarcoma. The tumor was surgically resected and was easily separated from the surrounding tissues. Nevertheless, a local recurrence developed 43 days after the operation, and the patient's condition deteriorated rapidly. Hepatomegaly and ascites believed to represent the Budd-Chiari syndrome were noted. The patient died on the 163rd postoperative day. Autopsy revealed a tumor extending from the inferior vena cava just above the right renal vein to the right atrium and involving the lobus caudatus of the liver. Clinically, the tumor was thought to have arisen from the middle segment of the inferior vena cava. However, a diagnosis of primary hepatic rhabdomyosarcoma with extrahepatic growth could not be excluded. Only 12 cases of primary liver rhabdomyosarcoma have been reported, and none of those patients demonstrated Budd-Chiari syndrome. Our patient, diagnosed as rhabdomyosarcoma with secondary Budd-Chiari syndrome, is believed to be the first such report.(Internal: Medicine 32: 67-71, 1993)
- 社団法人 日本内科学会の論文
著者
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Fujita Hiroshi
The Department of Cardiology, Kyoto Second Red Cross Hospital
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SHIRONO Kouichi
the Department of Surgery, Ayabe Municipal Hospital
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KAWATA Kouichi
the Department of Internal Medicine, Ayabe Municipal Hospital
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SAWADA Takahisa
the Department of Internal Medicine, Ayabe Municipal Hospital
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MIZUTANI Takaaki
the Department of Internal Medicine, Ayabe Municipal Hospital
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IWASAKI Yasushi
the Department of Surgery, Ayabe Municipal Hospital
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KOUNOSU Hiroshi
the Department of Surgery, Ayabe Municipal Hospital
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SHIRKATA Shuji
the Department of Surgery, Ayabe Municipal Hospital
関連論文
- PJ-654 Risk Factors of Cardiac Rupture after Acute Myocardial Infarction(PJ110,ACS/AMI (Clinical/Pathophysiology) 1 (IHD),Poster Session (Japanese),The 73rd Annual Scientific Meeting of The Japanese Circulation Society)
- Rhabdomyosarcoma in the Inferior Vena Cava with Secondary Budd-Chiari Syndrome.