QT Prolongation and Syncopal Attacks A Case of the Romano-Ward Syndrome

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概要

• 論文の詳細を見る

• The Romano-Ward syndrome is very rare as hereditary disease. Only 5 families have been reported in Japan before the present report. The patient, a 15-year-old female, had been treated for epilepsy due to syncopal attacks. Electrocardiography revealed occurrence of an augmented and labile U wave and prolongation of the Q-T interval, with recordings of frequent multifocal extrasystoles and transient ventricular fibrillation. Also noticed was sinus bradycardia. Clinical examinations presented no results coinciding with those specific ECG findings. It was inferred through surveys of her family tree that the present case had an autosomal dominant trait, heterozygously affected through the male line. Severe arrhythmias detected on her ECGs were suppressed by oral administration of 30 mg/day propranolol. Judging from the fact, propranolol may be the first to be administered among a variety of anti-arrhythmic agents in the Romano-Ward syndrome.

• International Heart Journal刊行会の論文

著者

• HANAZONO Naoto

  Department of Internal Medicine, Tottori University School of Medicine

• TANAKA Ryotaro

  Clinic of Internal Medicine, Tottori Prefectural Central Hospital

関連論文

• Prinzmetals Angina Pectoris with Normal Coronary Arteriograms
• Heritable Q-T Prolongation without Deafness : The Romano-Ward Syndrome
• QT Prolongation and Syncopal Attacks A Case of the Romano-Ward Syndrome

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