An Adult Case with Hunters Syndrome Presenting Prominent Hepatic Failure: Light and Electron Microscopic Features of the Liver
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概要
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We describe a 40-year-old male patient with Hunters syndrome. His main manifestations were ascites and esophageal varices due to cirrhotic liver. We obtained hepatic biopsy samples and examined them. Ultrastructurally, the features of the hepatocytes and Kupffer cells were the same as those reported in young patients. The passage of 40 years led to gradual progression to fibrosis, and ultimately liver cirrhosis. Namely, with a longer survival time, the complications of liver cirrhosis become more remarkable. Hepatic fibrosis in Hunters syndrome is slowly progressive and patients who are expected to have a longer life span should be continuously monitored for hepatic complications.
- 社団法人 日本内科学会の論文
著者
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Enjoji Munechika
Department Of Clinical Pharmacology Faculty Of Pharmaceutical Sciences Fukuoka University
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Kotoh Kazuhiro
Department Of Medicine And Bioregulatory Science Graduate School Of Medical Sciences Kyushu Universi
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Nakamuta Makoto
Department Of Fukuoka University
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Yoshimoto Tsuyoshi
Department Of Gastroenterology Kyushu Medical Center National Hospital Organization
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Morizono Shusuke
Department Of Medicine And Bioregulatory Science Graduate School Of Medical Sciences Kyushu Universi
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Kohjima Motoyuki
Department Of Gastroenterology Kyushu Medical Center National Hospital Organization
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Nakamuta Makoto
Department of Medicine and Bioregulatory Science, Graduate School of Medical Sciences, Kyushu University
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Sakai Hironori
Liver Center, National Hospital Kyushu Medical Center
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Miyagi Yuzuru
Department of Medicine and Bioregulatory Science, Graduate School of Medical Sciences, Kyushu University
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