A Case of Autoimmune Hepatitis Associated with Veno-occlusive Disease and Primary Sclerosing Cholangitis

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概要

• 論文の詳細を見る

• 53歳の女性が肝障害で当科入院した.血液生化学検査,肝生検より自己免疫性肝炎,細小肝静脈閉塞性疾患の合併を認めた.さらに内視鏡的逆行性膵胆管造影で原発性硬化性胆管炎と診断した.プレドニゾロンとウルソデオキシコール酸により臨床所見ならびに検査所見は改善した.本症例は自己免疫性肝炎,細小肝静脈閉塞性疾患さらに原発性硬化性胆管炎と異なる3肝疾患の要素が見られた.何らかの免疫学的関与が疑われ,自己免疫性肝疾患の病態を考える上で貴重な症例と思われ報告する.A 53-year-old woman was admitted to our hospital because of liver dysfunction. Laboratory data and liver biopsy revealed autoimmune hepatitis (AIH) and veno-occulusive disease (VOD). Endoscopic retrograde cholangiopancreatography demonstrated bile duct changes consistent with primary sclerosing cholangitis (PSC). The clinical features and liver profile tests improved with predonisolone and ursodeoxycluic acid. This patient is a rare case initially presenting features of 3 different hepatic diseases; AIH, VOD and PSC. During her long clinical course, predonisolone was effective. This case may provide an insight in understanding autoimmune hepatic diseases.

• 東京女子医科大学学会の論文

著者

• Kamatani N

  Tokyo Womens Medical Univ. Tokyo Jpn

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• A Case of Autoimmune Hepatitis Associated with Veno-occlusive Disease and Primary Sclerosing Cholangitis
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