Congenital Atresia of Unilateral Pulmonary Veins Associated With a Single Ventricle : A Rare Case Report and Literature Review
スポンサーリンク
概要
- 論文の詳細を見る
Congenital atresia or extreme hypoplasia of individual pulmonary veins is a rare condition that is usually asymptomatic if it only involves 1 or 2 segments of the lungs. It may be fatal if it occurs in combination with other complex cardiac defects. The patients often present with recurrent pulmonary infections, hemoptysis, or cyanosis in the latter case. A definitive diagnosis can be made by cardiac catheterization with selective pulmonary wedge angiography. The treatment of this condition is a challenge and is controversial, and the prognosis is usually poor. We describe the case of a male infant who suffered from shortness of breath and cyanosis since birth. On echocardiography and cardiac catheterization, he was found to have a complex congenital heart disease with a single ventricle (right ventricle morphology), mitral atresia, large atrial septal defect, and atresia of the right pulmonary veins; severe pulmonary hypertension was also observed. He underwent pulmonary artery banding at the age of 2.5 months, but he died because of a pulmonary infection at the age of 6 months. In this report, we present this rare case and review the previous literature.
- 社団法人日本循環器学会の論文
- 2008-08-20
著者
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LEE Pi-Chang
Division of Cardiology, Department of Medicine, Taipei Veterans General Hospital
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Lee Pi-chang
Division Of Cardiology Department Of Medicine Taipei Veterans General Hospital
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Lee Pi-chang
Division Of Pediatric Cardiology Taipei Veterans General Hospital:national Yang-ming University
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Jan Sheng-ling
Division Of Pediatric Cardiology Taichung Veterans General Hospital
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Hwang Betau
National Yang-ming University:department Of Pediatrics Taipei City Hospital Zhongxiao Branch
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Lee Hsing-Yuan
Department of Pediatrics, Taoyuan Armed Force General Hospital
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Meng C.C.Laura
Division of Pediatric Cardiology, Taipei Veterans General Hospital
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Lee Hsing-yuan
Department Of Pediatrics Taoyuan Armed Force General Hospital:department Of Biological Science And T
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Meng C.c.laura
Division Of Pediatric Cardiology Taipei Veterans General Hospital:national Yang-ming University
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Jan Sheng-ling
Division Of Cardiology Department Of Pediatrics Taichung Veterans General Hospital
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- The Impact of Diastolic Dysfunction on the Atrial Substrate Properties and Outcome of Catheter Ablation in Patients With Paroxysmal Atrial Fibrillation
- Congenital Atresia of Unilateral Pulmonary Veins Associated With a Single Ventricle : A Rare Case Report and Literature Review
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