小児機能性縦隔 Paraganglioma の1例

概要

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An 11-year-old boy who complained of general fatigue and displayed signs of hypertension was admitted to our hospital. Chest X-ray, CT scan and MRI revealed a tumor in the post-mediastinum. His serum and urine catecholamines, renin and aldosterone were elevated. We diagnosed the patient as having a functioning paraganglioma, and treated his hypertension with prazosin-HCI until surgery. On thoracotomy a 5×3×2.5cm mass was resected, and the diagnosis of paraganglioma was confirmed by histopathological findings. After the operation, the patient no longer required antihypertensive agents. Four years after the surgery he is doing well with no evidence of recurrence. Mediastinal paraganglioma is relatively rare in children. Twenty-six cases of juvenile paraganglioma have been reported in japan. In 21 cases it occurred in the retroperitoneal region, while in only 4 (14.8%), including our patient, it occurred in the mediastinal region.
特定非営利活動法人日本小児外科学会の論文
1992-10-20