胸壁原発悪性小細胞腫瘍(いわゆるAskin腫瘍)の1例

概要

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A 6-year-old girl of the malignant small cell tumor of the thoracopulmonary region in childhood so called "Askin tumor" was presented. She had a huge mass occupying the left thorax. Total resection of the mass with combined excision of 7th and 8th ribs was performed. The defect of the chest wall was reconstructed with silastic cheet. Histological examination showed the small round cell, with PAS positive, hyperchromic nuclei, scanty cytoplasm and frequently presented nucleoli. Mitotic figures were also frequently seen. Homer-Wright rosette were present, though scanty in numbers, and immunohistichemical reactivity for NSE was positive. Immunostaining of Desmin, Myoglobin, LCA were all negative. After operation she received irradiation chemotherapy, and is currently free of disease for 12 months.
日本小児外科学会の論文
1987-06-20