閉鎖部より肛門側が aganglionic であった回腸閉鎖の1例

概要

論文の詳細を見る
We have experienced a case of ileal atresia associated with total colon aganglionosis. The dianosis was initially made by histological observation of aganglionosis in the resected distal ileum and colon. Aganglionosis was found in the entire bowel distal to the atresia while the proximal bowel was normal. Etiology and pathogenesis of the association of ileal atresia with aganglionosis were discussed. The association of intestinal atresia with aganglionosis is very rare. No more than 14 cases have been found in the reports as far as we could determine. Five patients similar to ours have been reported. Three of these 6 cases including ours were complicated with malrotation and one with meconium peritonitis. These complications might have caused vascular accident, which may have interfered of the intramural ganglions from the oral to the anal direction at the early intrauterine life. It is doubtful, however, that all cases had vascular accident at the oligoganglionic segment.
日本小児外科学会の論文
1982-12-20