Two Cases of Recklinghausen's Disease with Neurofibroma and Bony Changes in the Oral Cavity.

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In 1882, Recklinghausen first described multiple neurofibromatosis as a disease charactesized by tumors of the skin and peripheral nerves. Recklinghausen's neurofibromatosis is an autosomal dominant inherited syndrome defined. by the presence of multiple cafe-au-lait spots, benign neurofibroma. Oral involvement is unusual in cases of von Recklinghausen's neurofibromatosis. Although the most obvious lesions occur on the skin, deeper structures also may be affected including the kidney, bladder, larynx, heart and central nervous system. Clinical manifestations are protean, many being clearly related to the local effects of the neurofibroma, but others having a less certain origin.<BR>We experienced two patients who had been referred to our clinic for exact examination of intraoral swelling. They were both histopathologically diagnosed von Recklinghausen's disease associated with oral lesion.
特定非営利活動法人日本口腔科学会の論文