Urine production in a case of atypical fetal polycystic kidney disease. A case report.:A case report

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We recently experienced a case of atypical fetal polycystic kidney disease (IPKD). This case showed reduced amniotic fluid and fetal urine production at 30 weeks of gestation. The mother was admitted to our hospital. During admission, the sonographic findings for the fetus demonstrated a normal appearing bladder, oligohydramnios, bilateral hyperechoic kidney (not enlarged), and reduced fetal urine production.<BR>These findings suggested a diagnosis of atypical fetal polycystic kidney disease. Cesarean section was performed at 40weeks of gestation due to fetal distress. The male newborn, who weighed 2770 grams, had an Apgar score of four at 1 min and five at 5 min. Bilateral pneumothorax occurred in the newborn immediately after birth, and there was a marked reduction in renal function from day 7 after birth. USG demonstrated many polycystic regions (5-10mm), and the medulla was poorly separated from the renal sinus in the bilateral kidneys. Accordingly, the newborn was diagnosed as having IPKD. At present, 2 years after birth, the infant, who has been undergoing chronic hemodialysis, is well.
近畿産科婦人科学会の論文