Intraosseous Well-Differentiated Osteosarcome Arising from the Rib Case Report and Literature Review.

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Intraosseous well-differentiated osteosarcoma is a rare subtype of osteosarcomas and must be distinguished from benign tumorous conditions due to its similarity on preoperative clinical examination and from conventional osteosarcoma because of its much better prognosis. We now report a very rare case of intraosseous well-differentiated osteosarcoma, primarily occurring in the right third rib of a 9-year-old boy. The plain and CT scan films showed protruded tumor mass arising from the right third rib, and bone scinti scan film revealed marked high uptake. Histologically, the resected mass showed proliferation of short-fusiform or spindle-shaped cels with little nuclear atypia, intermingled with fibrous dysplasia-like immmature bone trabeculae in the medullary cavity. Moreover, the tumor mass continuously protruded into the extramedullary adjacent soft part with destruction of the cortex. These features are compatible with intraosseous well-differentiated osteosarcomas. Although the follow-up period is short, the patient is well with no local recurrence or distant metastasis.
西日本整形・災害外科学会の論文