ステロイド治療が奏効したCogan症候群の1例

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A 12-year-old female had iritis, episcleritis, papilledema and vestibuloauditory dysfunction. The diagnosis was atypical Cogans syndrome as described by Cody and Haynes.<BR>The initial symptoms were high fever and injected bulbar conjunctiva.<BR>Attack of vertigo, as in Ménières disease, appeared 2 months after the onset. The results of equilibrium and glycerol tests, and electrocochleography suggested endolymphatic hydrops in the inner ear.<BR>Within 4 weeks after the initiation of steroid therapy, hearing improved and ocular symptoms disappeared without papilledema. At the time of discharge, she had no ataxia, but bilateral CP was present in the caloric test.<BR>We considered that the disorder of the inner ear in Cogans syndrome is hydrops due to vascular insufficiency.