口蓋裂を伴つた咽頭舌奇形症例

概要

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A four years aged female with the new type of the congenital oro-pharyngeal malformations was reported.She was first seen by the authors because of speech disorders resembling to children with cleft palate.In this case, the membraneous funicle was located between the nasopharynx (on the mid-line and at the level of ostium of eustachian tube) and the roof of the tongue (on the mid-line and just in the front of papillae vallatae)through the clefted soft-palate without any adhesions to the retropharyngeal wall.The location of this membraneous funicle was embryologically consistent with the pharyngeal membrane formed in the early week embryo.Palato-plasty and removal of this malformed funicle were performed under general anaesthesia.Inside of thie mem.braneous funicle, the cartilage plate was found and it was histologically “Hyaline Cartilage”.Some embryological considerations on this case are as follows; This oro-pharyngeal membraneous funicle could be the remnants of the pharyngeal membrane.And the cartilage-plate inside of it could be explained by the persistence of the mesodermal remnants arround it as well as osseous atresia of choana maybe originated by the oro-nasal membrane formed by only ectoderm.And another complicated malformation of clefted soft-palate was maybe followed by this remnant of the pharyngeal membrane.