Intractable Skin Necrosis and Interstitial Pneumonia in Amyopathic Dermatomyositis, Successfully Treated with Cyclosporin A
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概要
- 論文の詳細を見る
We report a patient with amyopathic dermatomyositis (DM) who mainly showed interstitial pneumonia and intractable skin necrosis in bilateral elbows and soles with a poor response to immunomediated therapy, including corticosteroid and high-dose intravenous immunoglobulin. Soon after starting oral cyclosporin A (CyA) the skin lesions healed completely and the interstitial pneumonia promptly improved in parallel with a decrease in serum KL-6. Since fatal interstitial pneumonia is frequently associated with amyopathic DM as in this case, administration of CyA should be actively considered as a therapeutic option when clinical symtoms are progressive and resistant to conventional treatments.(Internal Medicine 42: 1253-1258, 2003)
- 社団法人 日本内科学会の論文
著者
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MATSUDA Masayuki
the Third Department of Medicine, Shinshu University School of Medicine
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HOSHI Kenichi
the Third Department of Medicine, Shinshu University School of Medicine
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Ikeda Shu-ichi
The Third Department Of Internal Medicine Shinshu University School Of Medicine
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ISHII Wataru
the Third Department of Medicine, Shinshu University School of Medicine
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Ishii Wataru
The Third Department Of Medicine Shinshu University School Of Medicine
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Matsuda Masayuki
The Third Department Of Medicine Shinshu University School Of Medicine
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Hashimoto Takao
The Third Department Of Internal Medicine Shinshu University School Of Medicine
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SHIMOJIMA Yasuhiro
The Third Department of Medicine, Shinshu University School of Medicine
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KATO Takashi
The Third Department of Medicine, Shinshu University School of Medicine
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TANAKA Yukio
The Department of Medicine, National Nagano Hospital
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