Spontaneous Regression of Peripheral Pulmonary Artery Stenosis in Williams Syndrome

元データ 1996-04-20 社団法人日本循環器学会

概要

An infant girl diagnosed with multiple peripheral pulmonary artery stenosis and Williams syndrome was followed-up for 17 years. Three cardiac catheterizations performed over the follow-up period showed that spontaneous gradual regression of the stenosis occurred with time. The initial systolic pressure gradient of 77-79 mmHg at the stenoses had decreased to 23-29 mmHg when measured at 17 years of age. Contrary to the progressive nature of systemic artery stenosis in Williams syndrome, peripheral pulmonary artery stenosis appears to have the capacity for spontaneous improvement. Careful consideration is required to determine the indications for interventional catheterization for the dilation of peripheral pulmonary artery stenosis in cases of Williams syndrome.

著者

Eguchi S Department Of Thoracic And Cardiovascular Surgery Niigata University School Of Medicine
Watanabe Hiroshi Department of Cardiology, Niigata City General Hospital
EGUCHI SHOJI Niigata University School of Medicine
EGUCHI SHOJI The 2nd Dep. of Surgery
Tatebe Shoh Department of Thoracic and Cardiovascular Surgery, Niigata University School of Medicine
Miyamura Haruo Department of Thoracic and Cardiovascular Surgery, Niigata University School of Medicine
Eguchi Shoji Department of Thoracic and Cardiovascular Surgery, Niigata University School of Medicine
Miyamura Haruo The Second Department of Surgery Niigata University School of Medicine
Miyamura Haruo Department Of Thoracic And Cardiovascular Surgery Niigata University School Of Medicine
Eguchi Shoji Department Of Cardiovascular Surgery Niigata Kobari Hospital
Eguchi Shoji The Second Department Of Surgery Of Niigata School Of Medicine
Eguchi Shoji Dept Of Thoracic And Cardiovascular Surgery Niigata University Hospital
Eguchi Shoji Second Department Of Surgery Niigata University School Of Medicine
Tatebe Shoh Department Of Thoracic And Cardiovascular Surgery Mito Saiseikai General Hospital
Eguchi Shoji Department Of Molecular Design And Engineering Nagoya University
Eguchi Shoji The 2nd Department Of Surgery Niigata University School Of Medicine
Watanabe Hiroshi Division Of Thoracic And Cardiovascular Surgery Niigata University Graduate School Of Medical And De
Watanabe Hiroshi Department Of Applied Chemistry And Bioengineering Graduate School Of Engineering Osaka City Univers
Eguchi Shoji Department of Applied Chemistry Faculty of Engineering Nagoya University

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