Spontaneous Regression of Peripheral Pulmonary Artery Stenosis in Williams Syndrome
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概要
- 論文の詳細を見る
An infant girl diagnosed with multiple peripheral pulmonary artery stenosis and Williams syndrome was followed-up for 17 years. Three cardiac catheterizations performed over the follow-up period showed that spontaneous gradual regression of the stenosis occurred with time. The initial systolic pressure gradient of 77-79 mmHg at the stenoses had decreased to 23-29 mmHg when measured at 17 years of age. Contrary to the progressive nature of systemic artery stenosis in Williams syndrome, peripheral pulmonary artery stenosis appears to have the capacity for spontaneous improvement. Careful consideration is required to determine the indications for interventional catheterization for the dilation of peripheral pulmonary artery stenosis in cases of Williams syndrome.
- 社団法人日本循環器学会の論文
- 1996-04-20
著者
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Eguchi S
Department Of Thoracic And Cardiovascular Surgery Niigata University School Of Medicine
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Watanabe Hiroshi
Department of Cardiology, Niigata City General Hospital
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EGUCHI SHOJI
Niigata University School of Medicine
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EGUCHI SHOJI
The 2nd Dep. of Surgery
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Tatebe Shoh
Department of Thoracic and Cardiovascular Surgery, Niigata University School of Medicine
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Miyamura Haruo
Department of Thoracic and Cardiovascular Surgery, Niigata University School of Medicine
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Eguchi Shoji
Department of Thoracic and Cardiovascular Surgery, Niigata University School of Medicine
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Miyamura Haruo
The Second Department of Surgery Niigata University School of Medicine
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Miyamura Haruo
Department Of Thoracic And Cardiovascular Surgery Niigata University School Of Medicine
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Eguchi Shoji
Department Of Cardiovascular Surgery Niigata Kobari Hospital
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Eguchi Shoji
The Second Department Of Surgery Of Niigata School Of Medicine
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Eguchi Shoji
Dept Of Thoracic And Cardiovascular Surgery Niigata University Hospital
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Eguchi Shoji
Second Department Of Surgery Niigata University School Of Medicine
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Tatebe Shoh
Department Of Thoracic And Cardiovascular Surgery Mito Saiseikai General Hospital
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Eguchi Shoji
Department Of Molecular Design And Engineering Nagoya University
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Eguchi Shoji
The 2nd Department Of Surgery Niigata University School Of Medicine
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Watanabe Hiroshi
Division Of Thoracic And Cardiovascular Surgery Niigata University Graduate School Of Medical And De
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Watanabe Hiroshi
Department Of Applied Chemistry And Bioengineering Graduate School Of Engineering Osaka City Univers
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Eguchi Shoji
Department of Applied Chemistry Faculty of Engineering Nagoya University
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